Infantile(desmoid-type) fibromatosis, which represents the childhood counterpart of musculoaponeurotic fibromatosis(abdominal or extra-abdominal desmoid), usually arises as a solitary mass in skeletal muscle or in the adjacent fascia, aponeurosis, or periosteum. It chiefly affects children from birth to 5 years of age and shows considerable variations in its morphological appearacne that range from primitive mesenchymal forms to lesions that closely resemble adult desmoids except for the less uniform pattern and greater degree of cellularity. This tumor is a rare benign, but potentially locally aggresive lesion that is best treated by wide local resection. It has been confused with congenital fibrosarcoma and other soft tissue malignant tumors. One case of infantile fibromatosis affecting left gluteal region is reported.
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